Although histologically benign, juvenile nasopharyngeal angiofibroma jna can cause significant morbidity and occasional mortality through aggressive submucosal spread to adjacent structures. Ppt juvenile nasopharyngeal angiofibroma powerpoint. Transnasal endoscopic resection of juvenile nasopharyngeal. Juvenile nasopharyngeal angiofibroma jna is a relatively rare tumor of the nasopharynx, comprising only 0. Juvenile nasopharyngeal angiofibroma is a benign but locally invasive tumor accounting for about 0. Magnetic resonance imaging findings ayse gul alimli, murat ucar, cigdem oztunali, koray akkan, oznur boyunaga, cagr. In 1906 chareau revived the interest in the study of juvenile nasopharyngeal angiofibroma. Vessels are thinwalled, lack elastic fibers, have absent or incomplete smooth muscle, and vary in appearance from stellate or staghorn to barely conspicuous because of stromal compression.
Juvenile nasopharyngeal angiofibromas jna are a rare benign, but locally aggressive, vascular tumor. Nasopharyngeal angiofibroma an overview sciencedirect. We had recently a case of an extensive jna in the r nasal cavity extending from the anterior nares to the nasopharynx involving the rt pterygopalatine. Juvenile nasopharyngeal angiofibroma jna is a rare tumor that predominantly occurs in adolescent males, the average age of occurence being 15.
Tumor juga lebih sering meluas ke arah sinus sphenoid dan agak jarang ke arah sinus. This is a histologically benign lesion with very aggressive local behavior. It is a rare, benign, vascular neoplasm that accounts for less than 0. Introduction uncommon, benign and extremely vascular tumour up to 0.
The treatment for juvenile nasopharyngeal angiofibroma is questionable. Jnas represent less than 1 % of head and neck tumors. Angiofibroma of septal is a rare extra nasopharyngeal angiofibroma and has the. Nasopharyngeal angiofibroma is a histologically benign but locally aggressive vascular tumor of the nasopharynx that arises from the superior margin of the sphenopalatine foramen and grows in the back of the nasal cavity. Mar 07, 2020 it most commonly affects adolescent males and may grow into fissures of the. Typical signs are nasal and eustachian tube obstruction, adenoidal speech, and dysphagia. The tumor is locally aggressive and can invade into surrounding structures and cause significant complications. Angiofibroma nasofaring belia anb merupakan tumor jinak.
Angiofibroma nasofaring belia pdf juvenile nasopharyngeal angiofibroma is a pathologically benign yet locally aggressive and destructive vascular lesion of head and neck. Adolescents and young adults between 14 and 25 years are affected, and there is a distinct male predominance. Pdf juvenile nasopharyngeal angiofibroma researchgate. However, the extensions of the tumor seem to be independent, each one with distinct behavior. Juvenile nasopharyngeal angiofibroma has been documented since the time of hippocrates 4 bc. Angiofibroma nasofaring juvenile free download as pdf file. Imaging in the diagnosis of juvenile nasopharyngeal angiofibroma article pdf available in journal of clinical imaging science 3suppl 1. It is almost exclusicely encountered in adolescent males 1. Juvenile nasopharyngeal angiofibroma jna is a histologically. Evolution of management article pdf available in international journal of pediatrics 201222. Surgical approaches to juvenile nasopharyngeal angiofibroma. In the general population, jna occurs at an incidence of roughly 1.
The most common presenting symptom is painless nasal obstruction or epistaxis. Juvenile nasopharyngeal angiofibroma radiology reference. It most commonly affects adolescent males and may grow into fissures of the. Pdf this is a retrospective study that aimed to examine the outcomes of patients presenting with juvenile nasopharyngeal angiofibroma jna at a. Infact hippocrates goes on to describe a polyp in the nose which weeped blood. Download fulltext pdf download fulltext pdf juvenile angiofibroma.
Abstrak angiofibroma nasofaring adalah tumor jinak nasofaring yang secara histopatologis merupakan tumor jinak, tetapi secara klinis bersifat destruktif. Tumor ini sering terjadi pada lakilaki prepubertas dan remaja, jarang ditemukan pada pasien. This is a classical presentation of juvenile nasopharyngeal angiofibroma. These tumors are benign, however they are locally invasive. Juvenile nasopharyngeal angiofibroma knowledge for medical. The tumor usually arises in puberty and is more common in boys than in girls. Juvenile nasopharyngeal angiofibroma is a rare benign tumour of vascular origin found in adolescent males, originating around the sphenopalatine foramen.
Jna berasal dari posterolateral nasofaring di daerah fossa pterygopallatine. It is the most common benign tumor of the nasopharnyx but only accounts for less than 0. Shaheen in 1930 reported the first female patient with juvenile nasopharyngeal. Sep 01, 2008 juvenile nasopharyngeal angiofibroma is a rare, benign tumor that occurs most often in adolescent males. It most commonly affects adolescent males because it is a hormonesensitive tumor. Juvenile nasopharyngeal angiofibroma jna is a rare benign tumor arising predominantly in the nasopharynx of adolescent males. Well circumscribed but unencapsulated polypoid fibrous mass, bleeds severely on manipulation and biopsy, may occlude nares. Juvenile angiofibroma is a noncancerous growth that causes bleeding in the nose and sinuses. Study the changing trend basically in the northeastern region of southeast asia and its. Although the exact pathogenesis of the tumour is not yet known, natural history and growth patterns can be predicted.
Although rare cases have been reported in females, the tumor has such a strong male. We report the case of a 17yearold male who presented in 1995 with a mass filling the left posterior nasal cavity. Jnas originate from the posterior choanal tissues and rapidly extend into the surrounding regions, including the nasopharynx, the orbits, and even the intracranial cavity. Oct 18, 2018 juvenile nasopharyngeal angiofibroma jna is an uncommon, benign tumor of the nose that is generally seen in boys. Juvenile nasopharyngeal angiofibromas occur almost exclusively in males and usually in adolescence 15 years. Recently a changing trend has been seen in its epidemiology, pathogenesis, diagnosis, medical management, preoperative care, surgical management and postoperative care including radiotherapy. Intricate mixture of stellate and staghorn blood vessels with variable vessel wall thickness ranging from single layer of endothelium to variable smooth muscle coat. Juvenile nasopharyngeal angiofibroma with orbital extension angiofibroma nasofaringeo juvenil con extension orbitaria. May 16, 2018 juvenile nasopharyngeal angiofibroma jna occurs exclusively in males. Nasoangiofibroma youth is a highly vascularized tumor almost exclusively male adolescents presentation. Although the use of nonsurgical therapies is described in the literature, surgery is currently considered the ideal treatment for. Tumor ini memiliki histopatologi yang sama dengan angiofibroma nasofaring.
Juvenile nasopharyngeal angiofibroma jna is a benign vascular tumor that appears in the nasal cavity. Pdf juvenile nasopharyngeal angiofibroma in a tertiary centre. Preoperative selective arterial embolization has decreased intraoperative blood loss and facilitated resection of larger tumors. The first description of this tumour dates from nucci et al. View of angiofibroma nasofaring pada pasien usia lanjut. Nasopharyngeal angiofibroma definition of nasopharyngeal. Juvenile nasopharyngeal angiofibroma jna javiers story. May 05, 20 greetings from gv ent centre, kochi, india.
Nasopharyngeal angiofibroma introduction juvenile nasopharyngeal angiofibroma jna is a benign, but locally aggressive and extremely vascular head and neck neoplasm, occurring almost exclusively in the nasopharynx of adolescent males. Jna can spread into a variety of compartments in the head including the sinuses, the orbit where the eye is located, and the brain which can make. Surgery is preferred among all, but it is difficult to be performed because of vascular component of tumor and because of lesion extension and exposure. Juvenile nasopharyngeal angiofibroma with audio youtube. May 16, 2018 nasopharyngeal angiofibroma is usually encapsulated and composed of vascular tissue and fibrous stroma with coarse or fine collagen fibers.
Transnasal endoscopic resection of juvenile nasopharyngeal angiofibroma without preoperative embolization. Juvenile nasopharyngeal angiofibroma a free powerpoint ppt presentation displayed as a flash slide show on id. They often grow quickly during puberty, then slow down or stop growing entirely after adolescence. Return to article details angiofibroma nasofaring pada pasien usia lanjut download download pdf. Juvenile nasopharyngeal angiofibroma jna is a rare tumor that exhibits a predictable spreading pattern. The juvenile nasopharyngeal angiofibroma jna is a highly nasoangiofibroma youth is a highly vascularized tumor almost exclusively male.
Mulheres, sexualidade e a igreja catolica by uta rankeheinemann. Diagnosis dan penatalaksanaan angiofibroma septum nasi jurnal. Review article nasopharyngeal angiofibroma ashutosh hota s. Jul 19, 2015 cellular angiofibroma ca represents a quite recently described mesenchymal tumour that occurs in both genders, in particular in the vulvovaginal region in women and in the inguinoscrotal area in men. Pdf imaging in the diagnosis of juvenile nasopharyngeal. Although it is nonmalignant not cancerous, it can expand quickly and extensively. Bedah sinonasal endoskopik angiofibroma nasofaring belia. Jul 15, 2015 juvenile nasopharyngeal angiofibroma jna is a benign neoplasm of the nasopharynx. Juvenile nasopharyngeal angiofibroma jna is a rare, benign, but locally aggressive tumor occurring almost exclusively in adolescent males. Juvenile nasopharyngeal angiofibroma jna springerlink. Juvenile nasopharyngeal angiofibroma electronic journal of.
Juvenile nasopharyngeal angiofibroma jna is a histologically benign vascular tumor that arises in boys between the ages of 12 and 15 years, with only rare cases reported in patients younger than 10 or older than 25. Nasopharyngeal angiofibroma is a benign, vascular, polypoid fibrous mass in located in the the posterolateral wall of the nasal cavity. Angiofibroma nasofaring juvenil perhimpunan onkologi radiasi. Doc lapsus angiofibroma nasofaring anggy novitasari.
The juvenile nasopharyngeal angiofibroma has a characteristic growth in all directions from its origin. Health, general endoscopic surgery complications and side effects patient outcomes endoscopy nasopharyngeal cancer care and treatment diagnosis risk factors. The typical patient is an adolescent male with a clinical history of recurrent epistaxis and nasal obstruction. Jan 08, 2018 javier and his family share their experience at johns hopkins medicine, after seeking treatment following a diagnosis of a juvenile nasopharyngeal angiofibroma jna tumor. Juvenile nasopharyngeal angiofibroma is a locally aggressive benign vascular neoplasm, composed of vasogenic and myofibroblastic elements, accounts for 0. Sep 16, 2015 juvenile nasopharyngeal angiofibroma is a very rare, highly vascular, uncapsulated and locally invasive tumor. Juvenile nasopharyngeal angiofibroma jna is a rare, histologically benign skull base tumor that develops in adolescents and young adults, almost exclusively in males. Juvenile nasopharyngeal angiofibroma is a rare benign head and neck tumor in male adolescent, but has a high risk of invasion. A juvenile nasopharyngeal angiofibroma jna is a noncancerous tumor made up of blood vessels that grow at the posterior aspect of the nose. Jnas occur almost exclusively in the nasopharynx of adolescent. Juvenile nasopharyngeal angiofibroma boston childrens hospital. Common practice is to excise the tumor with open or endoscopic surgery. Juvenile angiofibroma is a rare benign lesion originating from the pterygopalatine fossa with distinctive epidemiologic features and growth patterns.1324 1482 1232 1340 710 475 552 884 764 1123 285 702 235 214 606 1144 1531 1087 1285 1383 1342 1199 99 193 570 1182 972 981 741 1346 721 323 462 971 911 1198 1321 315 366 281 1402 1070 641 448